Utilize este identificador para referenciar este registo: http://hdl.handle.net/10400.17/419
Título: Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association
Autor: Sarris, G
Giannopoulos, N
Tsoutsinos, A
Chatzis, A
Kirvassilis, G
Brawn, W
Comas, J
Corno, A
Carlo, D
Fragata, J
Hraska, V
Jacobs, J
Krupianko, S
Sairanen, H
Stellin, G
Urban, A
Ziemer, G
Palavras-chave: Distribuição por Idade
Anomalia de Ebstein
Válvulas Cardíacas
Ventrículos Cardíacos
Mortalidade Hospitalar
Modelos Logísticos
Análise Multivariada
Cuidados Paliativos
Estudos Retrospectivos
Resultado de Tratamento
Data: 2006
Editora: Elsevier
Citação: J Thorac Cardiovasc Surg. 2006 Jul;132(1):50-7. Epub 2006 Jun 2
Resumo: OBJECTIVE: Since most centers' experience with Ebstein anomaly is limited, we sought to analyze the collective experience of participating institutions of the European Congenital Heart Surgeons Association with surgery for this rare malformation. METHODS: The records of all 150 patients (median age 6.4 years) who underwent surgery for Ebstein anomaly in the 13 participating Association centers between January 1992 and January 2005 were reviewed retrospectively. Patients with congenitally corrected transposition were excluded. RESULTS: Most patients (81%) had Ebstein disease type B or C and significant functional impairment (61% in New York Heart Association class III or IV) and 16% had prior operations. Surgical procedures (n = 179) included valve replacement (n = 60, 33.5%), valve repair (n = 49, 27.3%), 1(1/2) ventricle repair (n = 46, 25.6%), palliative shunt (n = 13, 7.26%), and other complex procedures (n = 11, 6.14%). There were 20 hospital deaths (operative mortality 13.3%) after valve replacement in 5 patients, valve repair in 3, 1(1/2) ventricle repair in 7, palliative procedures in 3, and miscellaneous procedures in 2. Younger age and palliative procedures were univariate risk factors for operative death, but only age was an independent predictor on multivariable analysis. CONCLUSIONS: Most patients coming to surgery presented in childhood and were significantly symptomatic. More than half underwent valve replacement or repair, but a considerable proportion had severe disease necessitating 1(1/2) ventricle repair or palliative procedures. Operative mortality did not differ significantly among repair, replacement, and 1(1/2) ventricle repair but was associated with palliative procedures for severe disease early in life, young age being the only independent predictor of operative death.
Peer review: yes
URI: http://hdl.handle.net/10400.17/419
Aparece nas colecções:CCT - Artigos

Ficheiros deste registo:
Ficheiro Descrição TamanhoFormato 
JTCS 2006 50.pdf223,04 kBAdobe PDFVer/Abrir

FacebookTwitterDeliciousLinkedInDiggGoogle BookmarksMySpace
Formato BibTex MendeleyEndnote Degois 

Todos os registos no repositório estão protegidos por leis de copyright, com todos os direitos reservados.